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Abstract
Adrenoleukodystrophy (ALD) is an inheritable clinical disorder in which very long
chain fatty acids accumulate in several tissue types. ALD is underrepresented in the
psychiatric literature, although the disorder may cause an organic brain syndrome,
often misdiagnosed as another psychiatric problem. A survey of 109 reported cases
of ALD revealed that 39% presented with some psychiatric sign or symptom, whereas
17% presented exclusively as a psychiatric problem. A computed axial tomogram (CAT)
head scan is recommended to rule out ALD in psychiatric patients suspected of having
organic brain disease, as a characteristic image may be found in ALD patients who
have brain involvement.
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Article info
Publication history
Received in revised form:
February 7,
1987
Received:
July 18,
1986
Identification
Copyright
© 1987 Published by Elsevier Inc.
